Thoracic Insufficiency Syndrome
Also known as: TIS.
What is thoracic insufficiency syndrome?
The thorax is the portion of the body between the neck and abdomen that includes the spine, and ribs, sternum (breastbone), the chest wall (rib cage), and lungs. TIS is a rare congenital (before birth) complex condition that involves chest wall abnormalities which prevent normal lung growth or breathing.
What causes thoracic insufficiency syndrome?
Thoracic insufficiency syndrome commonly occurs with progressive curvature of the spine (scoliosis) but also with congenital absence of ribs, from spinal muscular atrophy, spina bifida and many other conditions.
What are the signs/symptoms of thoracic insufficiency syndrome?
Common symptoms may include a narrow trunk and rib cage, scoliosis (curved spine), absence of ribs or rib fusion, breathing problems and other symptoms.
What are thoracic insufficiency syndrome care options?
There may be options, however a common treatment is the surgical insertion of a device called a vertical expandable prosthetic titanium rib (VEPTR) that expands the chest and stabilizes the spine.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 8/7/2018 10:38:29 AM
From the Newsdesk
Growing up, Haley Gantt suffered from scoliosis. She had to wear a back brace to prevent her curve from worsening, but unfortunately, she was later told that a spinal fusion surgery would have to be considered because the brace had failed to prevent the curve from progressing. She fought hard and got through it. An accomplished basketball player, Haley is now on her way to playing Division II basketball for Biola University in Southern California.
Learn about Scoliosis with Dr. Stephen George, Pediatric Orthopedic Surgeon, at Nicklaus Children's Hosptial.