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Human molecular genetics,
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Molecular genetics and metabolism,
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Nature genetics,
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Human mutation,
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McGraw, C.M., Mahida, S., Jayakar, P., et al (2021). Uridine-responsive epileptic encephalopathy due to inherited variants in CAD: A Tale of Two Siblings.
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Nature genetics,
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Febres-Aldana, C., Pelaez, L. ..., Jayakar, P., et al (2020). A Case of UDP-Galactose 4'-Epimerase Deficiency Associated with Dyshematopoiesis and Atrioventricular Valve Malformations: An Exceptional Clinical Phenotype Explained by Altered N-Glycosylation with Relative Preservation of the Leloir Pathway.
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Cheng, H., Dharmadhikari, A.V., Varland, S., Ma, ..., Jayakar, P., et al (2018). Truncating Variants in NAA15 Are Associated with Variable Levels of Intellectual Disability, Autism Spectrum Disorder, and Congenital Anomalies.
American Journal of Human Genetics,
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Metz, K.A., Teng, X., Coppens, I., Lamb, H.M., Wagner, B.E., Rosenfeld, J.A., ..., Jayakar, P., et al (2018). KCTD7 deficiency defines a distinct neurodegenerative disorder with a conserved autophagy-lysosome defect.
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Hamilton, E.M.C., Tekturk, P., Cialdella, F., ..., MLC Research Group (2018). Megalencephalic leukoencephalopathy with subcortical cysts: Characterization of disease variants. .
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Chen, C.A., Bosch, D.G.M., Cho ScM, M.T., Rosenfeld, J.A., Shinawi, M., Lewis, R.A., Mann, J., ..., Jayakar, P., et al (2017). CORRIGENDUM: The expanding clinical phenotype of Bosch-Boonstra-Schaaf optic atrophy syndrome: 20 new cases and possible genotype-phenotype correlations.
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Epileptic Disorders,
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Kudr, M., Krsek, P., Maton, B., Malone, S., Jahodova, A., Komarek, V., Jayakar, P., et al (2016). Ictal SPECT is useful in localizing the epileptogenic zone in infants with cortical dysplasia.
Epileptic disorders,
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Russo, A., Lallas, M., Jayakar, P., Miller, I., Hyslop, A., Resnick, T., et al (2016). The diagnostic utility of 3D-ESI rotating and moving dipole methodology in the pre-surgical evaluation of MRI-negative childhood epilepsy due to focal cortical dysplasia.
Epilepsia,
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Russo, A., Jayakar, P., Lallas, M., Miller, I., Hyslop, A., Korman, B., Dunoyer, C., et al (2016). The diagnostic utility of 3D electroencephalography source imaging in pediatric epilepsy surgery.
Epilepsia,
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Bhoj, E.J., Li, D., Harr, M., Edvardson, S., ..., Jayakar, P., et al (2016). Mutations in TBCK, Encoding TBC1-Domain-Containing Kinase, Lead to a Recognizable Syndrome of Intellectual Disability and Hypotonia.
American journal of human genetics,
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Aggarwal, V., Dobrolet, N., Fishberger, S., Zablah, J., Jayakar, P., Ammous, Z. (2015). PRKAG2 mutation: An easily missed cardiac specific non-lysosomal glycogenosis.
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Krsek, P., Kudr, M., Jahadova, A., Komarek, V., Maton, B., Malone, S., Miller, I., Jayakar, P., Resnick, T., Duchowny, M. (2013). Localizing value of ictal SPECT is comparable to MRI and EEG in children with focal cortical dysplasia.
Epilepsia,
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Bhatia, S., Ahmad, F., Miller, I., Ragheb, J., Morrison, G., Jayakar, P., Duchowny, M. (2013). Surgical treatment of refractory status epilepticus in children.
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Krsek, P., Jahodova, A., Kyncl, M., Kudr, M., Komarek, V., Jezdik, P., Jayakar, P., Miller, I., Korman, B., Rey, G., Resnick, T., Duchowny, M. (2013). Predictors of seizure-free outcome after epilepsy surgery for pediatric tuberous sclerosis complex.
Epilepsia,
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Kudr, M., Krsek, P., Maton, B., Malone, S., Jahodova, A., Jezdik, P., Komarek, V., Miller, I., Jayakar, P., Resnick,T., Duchowny, M. (2013). Predictive factors of ictal SPECT findings in paediatric patients with focal cortical dysplasia.
Epileptic Disorder,
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Winters, K.A., Jiang, Z., Xu, W., Li, S., Ammous, Z., Jayakar, P., Wierenga, J.A. (2012). Re-assigned diagnosis of D4ST1-deficient Ehlers-Danlos syndrome (adducted thumb-clubfoot syndrome) after initial diagnosis of Marden-Walker syndrome.
American Journal of Medical Genetics. Part A,
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Spiliopoulos, M., Jayakar, P., Spiliopoulos, D. (2012). Facial dysmorphism and skin manifestations in a patient with inherited systemic hyalinosis.
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Brunetti-Pierri, N., Paciorkowski, A.R., Ciccone, R., ..., Jayakar, P., et al (2011). Duplications of FOXG1 in 14q12 are associated with developmental epilepsy, mental retardation, and severe speech impairment.
European Journal of Human Genetics,
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Kurt, B., Jaeken, J., Van Hove, J., Lagae, L., ..., Jayakar, P., et al (2010). A novel POLG gene mutation in 4 children with Alpers-like hepatocerebral syndromes.
Archives of Neurology,
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van der Knaap, M.S., Lai, V., Kohler, W., Salih, M.A., ..., Jayakar, P., et al (2010). Megalencephalic leukoencephalopathy with cysts without MLC1 defect.
Annals of Neurology,
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Wang, B.T., Hemmat, M., Jayakar, P., Boyar, F., Chan, P., El Naggar, M., Anguiano, A. (2010). Paternal mosaic inv(20) resulting in a recombinant chromosome 20 in two siblings.
Pediatrics International,
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Horvath, R., Kemp, J.P., Tuppen, H.A., Hudson, ..., Jayakar, P., et al (2009). Molecular basis of infantile reversible cytochrome c oxidase deficiency myopathy.
Brain,
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Morales, A., Wierenga, A., Cuthbert, C., Sacharow, S., Jayakar, P., Velazquez, D., Loring, J., Barbouth, D. (2009). Expanded newborn screening in Puerto Rico and the US Virgin Islands: education and barriers assessment.
Genetics in Medicine,
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Oshima, J., Magner, D.B., Lee, J.A., Breman, A.M., ..., Jayakar, P., et al (2009). Regional genomic instability predisposes to complex dystrophin gene rearrangements.
Human Genetics,
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Krsek, P., Maton, B., Jayakar, P., Dean, P., Korman, B., Rey, G., et al (2009). Incomplete resection of focal cortical dysplasia is the main predictor of poor surgical outcome.
Neurology,
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Bornstein, B., Area, E., Flanigan, K.M., Ganesh, J., Jayakar, P., et al (2008). Mitochondrial DNA depletion syndrome due to mutations in the RRM2B gene.
Neuromuscular Disorders,
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