Also known as: BPS, pulmonary sequestration, accessory lung.
What is bronchopulmonary sequestration?
When a fetus develops a cystic piece of nonfunctioning abnormal lung tissue either within a lung (intralobar sequestration) or next to it (extralobar- more common in boys) that is not connected to the body’s airways, its known as bronchopulmonary sequestration.
What causes bronchopulmonary sequestration?
The cause of the rare congenital abnormality of lung development that occurs before birth is unknown. It does not appear to be inherited from parents and does not run in families. Other congenital malformations may be present (10%).
What are the symptoms of bronchopulmonary sequestration?
Bronchopulmonary sequestration may be diagnosed prenatally and have no symptoms during the neonatal period. Later in early childhood children may present with multiple episodes of pneumonia and a chronic cough. If the sequestered cystic piece enlarges it can compress normal lung resulting in breathing and heart problems. Extralobar sequestration may present with gastrointestinal symptoms i.e feeding difficulties.
What are bronchopulmonary sequestration care options?
A bronchopulmonary sequestration is typically removed surgically a short time after the baby is born. Outcomes from the surgery are typically quite good.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 3/23/2018 2:17:25 PM
VACC Camp is a week-long sleep-away camp for children requiring ventilator assistance (tracheostomy ventilator, C-PAP, BiPAP, or oxygen to support breathing) and their families. Learn more.
Join us for a great day of golf, delicious dinner and exciting auction...all to benefit the children of VACC Camp. Learn more.
From the Newsdesk
The medications that an asthmatic child uses could have effects on the oral mucosa.
The moment Justin was born, his mother and father were faced with the most daunting and challenging experience any parent can imagine. Just hours after birth, Justin was airlifted to Nicklaus Children’s Hospital for more specialized pediatric care. Having been diagnosed with pulmonary atresia and tetralogy of Fallot, he required immediate attention before it was too late.