Nikaidoh Procedure

Also known as: aortic translocation, aortic root translocations, arterial switch procedure

What is Nikaidoh procedure?

Transposition of the great arteries (TGA) is a rare congenital heart defect where the connections between the heart and the aorta and pulmonary artery are reversed. In some cases, TGA is present along with two other heart defects, a ventricular septal defect (VSD) and left ventricular outflow tract obstruction (LVOTO). Nikaidoh procedure is an arterial switch procedure that can be used to correct TGA with VSD and LVOTO.

What happens during the procedure?

Nikaidoh procedure is a major open-heart surgery that is performed under general anesthesia and requires a multi-day stay in the hospital. It involves the removal and reimplantation of both major arteries that connect to the heart, as well as other heart repairs.

Is any special preparation needed?

Your child will likely need to undergo several diagnostic tests to determine if they are a candidate for Nikaidoh procedure. Your doctors may have other guidance depending on the specific nature of the procedure. For example, you may need to avoid food and medication for a period of time before the procedure.

What are the risk factors?

A Nikaidoh procedure is a major, complex procedure that does pose risks, so it’s important to discuss these risks and potential outcomes with your doctors. Despite the risks, in many cases it’s the best treatment option available for the infant with a congenital heart defect, and many children who have undergone the procedure go on to lead healthy, productive lives.

Reviewed by: David Kalfa, MD

This page was last updated on: June 26, 2026 03:04 PM