Hemitruncus

Also known as: hemitruncus arteriosus, pulmonary artery coming from the aorta, PACA, anomalous origin of the right pulmonary artery.

What is hemitruncus?

Normally, the pulmonary artery comes off the right ventricle of the heart and splits into two distinct branches to carry blood to the lungs. With this very rare heart abnormality (hemitruncus), the main pulmonary artery and one branch, typically the left, are found in the correct position, however the right one comes out of the ascending aorta.

What causes hemitruncus?

Hemitruncus is a congenital heart defect of unknown cause.

What are the symptoms of hemitruncus?

Babies with hemitruncus typically have trouble with worsening lung vascular disease and heart failure.This presents as trouble breathing, and poor feeding-weight gain, among other symptoms.

What are hemitruncus care options?

Most neonates/infants with hemitruncus are treated surgically.


Reviewed by: Jack Wolfsdorf, MD, FAAP

This page was last updated on: September 17, 2020 11:32 AM

Pediatric Cardiology: Heart Program

The Heart Program – a world leader in pediatric cardiology and cardiovascular surgery and the care of children with congenital heart disorders – serves as a beacon to families confronting the reality of a child or newborn with a heart defect.

Learn more

Upcoming Events

11th Annual Dr. Moises Simpser VACC Camp Golf Tournament

Date: Friday, October 09, 2020

Join us for a great day of golf, delicious dinner and exciting auction...all to benefit the children of VACC Camp. Learn more.

Learn more about

Congenital Heart Defects/Disease

Any unusual physical feature or health problem that is present at the birth of a baby is known as a birth defect or a congenital anomaly. Learn more