Also known as: Binder type, nasomaxillary hypolasia, maxillafacial dysplasia.
What is Binder syndrome?
Binder syndrome is a congenital disorder characterized by a flat, underdeveloped midface and nose. The jaw might also be affected, and the face may appear imbalanced.
What causes Binder syndrome?
The exact cause of Binder syndrome is unclear. It may be a genetic disorder, and it appears to run in families in some cases.
What are the symptoms of Binder syndrome?
The flattened midface is the primary symptom of Binder syndrome. This may result in a recessed upper jaw and misaligned teeth (malocclusion). When the nose is affected, it is characterized by a flat nasal bridge and a short columella.
What are Binder syndrome care options?
Treatment for Binder syndrome will vary depending on what specific abnormalities are present. Reconstructive surgery may be an option to help with issues related to the face. Typically, correction of the recessed upper jaw is performed when the facial bones have finished growing, around 16-18 years of age, with a procedure known as LeFort I advancement. This is usually preceded and followed by orthodontic treatment.
The nasal deformity can be corrected around the same time with a septorhinoplasty and placement of a bone graft.
This page was last updated on: September 11, 2019 03:40 PM
Date: Friday, July 10, 2020
Nicklaus Children’s Hospital invites you to attend a conference designed to provide individuals with Beckwith-Wiedemann Syndrome (BWS) and their families with up-to-date information about the possible aspects of BWS and their management.