Organic Acid Quantitation (Succinylacetone)

Also known as: urinary organic acids: isolation and quantitation, metabolic analysis profile.

What is organic acid quantitation - succinylacetone?

Organic acid quantitation - succinylacetone is a test that can help diagnose a rare genetic disorders known as tyrosinemia type 1. The test measures the levels of an organic acid known as succinylacetone in the urine. High levels of urine succinylacetone are usually a sign of tyrosinemia type 1.

What happens during the procedure?

A sample of urine is required for organic acid quantitation. The sample is then sent to a laboratory for further testing and analysis.

Is any special preparation needed?

The patient may need to fast for several hours before giving a urine sample.

What are the risk factors?

There are no risk factors related to this test.

Reviewed by: Sajel L Kana, MD

This page was last updated on: April 22, 2021 04:23 PM

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Biochemical Genetic Test: Urine Organic Acids

Metabolism is the sum of the chemical processes whereby the body builds new molecules and breaks down others to get rid of waste products and produce energy. Learn more

Organic Acid Quantitation

Organic acid quantitation is a test that can help identify a number of genetic disorders that impact metabolism. Learn more