Organic Acid Quantitation (Succinylacetone)

Also known as: urinary organic acids: isolation and quantitation, metabolic analysis profile.

What is organic acid quantitation - succinylacetone?

Organic acid quantitation - succinylacetone is a test that can help diagnose a rare genetic disorders known as tyrosinemia type 1. The test measures the levels of an organic acid known as succinylacetone in the urine. High levels of urine succinylacetone are usually a sign of tyrosinemia type 1.

What happens during the procedure?

A sample of urine is required for organic acid quantitation. The sample is then sent to a laboratory for further testing and analysis.

Is any special preparation needed?

The patient may need to fast for several hours before giving a urine sample.

What are the risk factors?

There are no risk factors related to this test.

Reviewed by: Sajel L Kana, MD

This page was last updated on: December 18, 2020 05:24 PM

Learn more about