Also known as: neurofibromatosis.
What is plexiform neurofibroma?
Plexiform neurofibromas are a rare, benign (non-cancerous) form of tumor that can occur almost anywhere in the body, such as the face, arm, back, chest, legs and elsewhere. They are a symptom of neurofibromatosis; tumors form on nerve tissue. Unlike other tumors that occur with the disease, plexiform neurofibromas tend to be larger and more extensive.
What causes plexiform neurofibroma?
Plexiform neurofibromas are almost always the result of neurofibromatosis. This disease is most commonly a genetic disorder that is passed from parents to children.
What are the symptoms of plexiform neurofibroma?
The large, slow-growing tumors are the primary symptom of plexiform neurofibroma. These tumors can cause pain, and as they grow, they can negatively impact other parts of the body and even cause disfigurement in some instances.
What are plexiform neurofibroma care options?
In most cases, surgery to remove the tumor is the primary treatment of plexiform neurofibroma. New drugs are under evaluation for their ability to slow the growth of the tumors.
Reviewed by: Aaron J. Berger
This page was last updated on: 6/21/2019 2:26:47 AM
Date: Friday, July 10, 2020
Nicklaus Children’s Hospital invites you to attend a conference designed to provide individuals with Beckwith-Wiedemann Syndrome (BWS) and their families with up-to-date information about the possible aspects of BWS and their management.