Also known as: no ear, absence of the ear, ear malformations.

What is anotia?

Anotia is a rare congenital disorder in which the visible portion of the ear (external ear) is completely missing at birth. It can affect one or both ears.

What causes anotia?

The exact cause of anotia is not entirely clear. It may be related to the expecting mother being exposed to certain prescription or recreational drugs or having certain nutritional deficiencies. It can also occur as part of a genetic syndrome.

What are the symptoms of anotia?

Usually with anotia, the inner ear is unaffected. Affected babies can also have defects of the ear canal and the middle ear. Hearing can therefore be impaired.

What are anotia care options?

The external ear can be surgically reconstructed in children with anotia. Hearing can be improved with a hearing aid or in some cases, with surgical reconstruction of the ear canal.

Reviewed by: Saoussen Salhi, MD

This page was last updated on: 7/4/2018 9:54:35 AM

Upcoming Events

Beckwith-Wiedemann Syndrome (BWS) Family Conference

Nicklaus Children’s Hospital invites you to attend a conference designed to provide individuals with Beckwith-Wiedemann Syndrome (BWS) and their family’s up-to-date information about the possible aspects of BWS and their management. 

Learn more and register

From the Newsdesk

Movie Event Celebrates Children with Craniofacial Differences
04/30/2018 — Children who receive care at the Craniofacial Center at Nicklaus Children’s, along with their families, enjoyed an afternoon of red carpet glamour and photo booth fun on April 28. 
March Patient of the Month: Theodore
03/15/2018 — Meet our March Patient of the Month, Theodore. Theodore was diagnosed with cleft palate, cleft lip and a heart problem when he was only 18 weeks old. After he was born, Theodore had to be admitted into the NICU to be able to perform the necessary surgeries for him to live a healthy life.


Chad Perlyn, MD is a pediatric plastic surgeon and Co-Director of the operating room at Nicklaus Children's Hospital.