Desmoplastic Small Round Cell Tumor

Also known as: DSRCT, DSRCTs, small blue round cell tumor

What are desmoplastic small round cell tumors?

Desmoplastic small round cell tumors are a rare form of sarcoma, a type of cancer, that frequently impacts the abdomen or the pelvic area. When they do occur, it’s most commonly in male teenagers or young men.

What causes desmoplastic small round cell tumors?

Like most cancers, the root cause of desmoplastic small round cell tumors is due to changes in a cell’s DNA. What specifically causes this change to occur in regard to desmoplastic small round cell tumors isn’t clear.

What are the symptoms of desmoplastic small round cell tumors?

Common symptoms that can occur with desmoplastic small round cell tumors include abdominal pain and swelling, constipation or difficulty urinating.

How can desmoplastic small round cell tumors affect children?

Desmoplastic small round cell tumors occur most frequently in children or young adults. The condition primarily affects boys more than girls.

What are desmoplastic small round cell tumor treatments?

Surgery, chemotherapy, radiation therapy and targeted therapy are all potential treatments for desmoplastic small round cell tumors. In many cases, a combination of treatments is used to eradicate the cancer.

Reviewed by: Maggie Fader, MD

This page was last updated on: November 03, 2023 03:19 PM