What is Kasabach-Merrit syndrome?

Also known as: KMS, Hemangiomas with thrombocytopenia

Kasabach-Merritt syndrome (KMS) is also known as “hemangiomas with thrombocytopenia.” It is a combination of hemangioma, thrombocytopenia, and coagulopathy. It is a rare disease of infancy in which the thrombocytopenia (decreased platelet count) results from the hemangioma trapping and activating platelets, which in turn promotes further growth of the vascular tumor.

Bleeding problems can ensue and may be life-threatening. Laboratory testing including blood counts and clotting studies are important, as well as imaging studies and biopsy of the tumor when necessary.

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This page was last updated on: 1/29/2019 3:21:13 PM