Also known as: juvenile scleroderma, localized scleroderma.
What is scleroderma?
Scleroderma (hard skin) is a rare autoimmune disease where normal skin (usually, though other organ systems may be involved) is replaced by dense thick scar like tissue. There are two types-Localized scleroderma (common in children, particularly girls) which may present as bands of thick white tissue or morphea-patches (with purple borders) in the skin plus damage to muscle, bones and joints, and Systemic scleroderma (sclerosis) which is rare in children, more severe and involves internal organs as well as the skin.
What causes scleroderma?
Scleroderma is an autoimmune disorder. This means that the body’s own immune system (which normally defends us against infections) mistakenly attacks and damages the body’s own tissues. It’s believed that a combination of genetic and environmental factors can lead to this disease.
What are the symptoms of scleroderma?
Common skin changes include loss of the skin's ability to stretch, swelling of hands and feet, the tightening of the skin with hardening lines or streaks, tight oval-shaped patches of skin anywhere on the body known as morphea, fatigue and muscle weakness.
What are scleroderma care options?
Many children with localized skin scleroderma can be managed with topical ointments or creams. In more severe instances, medications that suppress the body’s immune response may be required.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 10/15/2018 2:33:43 PM
From the Newsdesk
In observance of vascular birthmarks awareness month, The International Birthmarks Institute at Nicklaus Children’s Hospital held its first Vascular Birthmarks Conference at the hospital’s main campus on May 5th. The event brought together patients, families and medical professionals representing a range of specialties to present the latest in diagnosis, treatment and research related to birthmarks.
The Boynton Beach Care Center is the newest Nicklaus Children’s care location and offers a range of services for children from birth through 21 years of age.