Prune Belly Syndrome (Eagle-Barrett Syndrome)
Also known as: Eagle-Barrett syndrome, triad syndrome
What is prune belly syndrome?
Prune belly syndrome is a rare birth defect occurring usually in boys where infants have a triad (three) of abnormalities. These include absence/poor development of abdominal muscles, undescended testicles and a big bladder with problems with their urinary tract which makes it difficult for them to empty their bladders. Infants in addition may have many other birth defects (skeletal, lungs, intestines and heart with girls having abnormalities in their external genitalia).
What causes prune belly syndrome?
While the cause is unknown, there may be a genetic abnormality as other children in a family may have the same problem. Blockage in fetal life of the tube that drains the bladder may cause some of the bladder and urinary tract abnormalities.
What are the signs/symptoms of prune belly syndrome?
Along with the three signs/symptoms of an undeveloped wrinkly abdominal wall, urinary tract problems and undescended testicles, older children with prune belly syndrome may have recurrent urinary tract infection. Other birth defects that may occur with prune belly syndrome may cause a variety of other symptoms. Some infants may be stillborn or not survive for more than a few months.
What are prune belly syndrome care options?
Treatment varies and depends on the severity of the symptoms. Antibiotics and a number of different surgical options are available.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 10/31/2017 11:56:18 AM
From the Newsdesk
Nicklaus Children’s is among the first pediatric facilities in the region to offer robotic single-site incision surgery for children utilizing the da Vinci Xi® system. The technique offers a single incision minimally invasive surgical option for gallbladder or ovarian surgeries in children.
When Maddy was only 12 hours old, she was flown to Nicklaus Children’s Hospital to undergo the first of several surgeries to treat spina bifida, a congenital condition that affects the backbone and membranes around the spinal cord. Thanks to a multidisciplinary team approach, Maddy received coordinated care by an array of subspecialists.