Also known as: TA
What is Tricuspid Atresia?
In the normal heart, the tricuspid valve is the opening that controls the flow of blood between the right atrium (where the blood enters the heart) and the right ventricle (where the blood leaves for the lungs). Tricuspid atresia is a problem with the development of the right side of the heart where this valve has not developed, with a smaller than normal lower right pumping chamber (right ventricle). Because of this valve blockage to the flow of blood, the body receives blood with less oxygen in it than it needs. There is usually an associated hole between the right and left upper chambers of the heart (right atrium and left atrium) called an atrial septal defect.
What causes tricuspid atresia?
Tricuspid atresia is a defect that babies are born with (congenital birth defect). It is often present with other heart problems. The exact cause is not known.
What are the symptoms of tricuspid atresia?
Babies with tricuspid atresia will have a bluish or purple tint to their lips, skin and nails, shortness of breath, feed poorly, and be extremely fatigued.
What are tricuspid atresia care options?
Surgery is required to repair this defect as soon as possible. The baby may be given oxygen and a medicine called prostaglandin E1 to keep blood going to the lungs and require a breathing machine or ventilator before the surgery.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 6/12/2018 2:18:53 PM
From the Newsdesk
Naialee Perez had just given birth to her first child, a baby boy named Liam, when a category five hurricane was making its way towards her hometown in the island of Puerto Rico. Liam was on a ventilator and undergoing treatment for a congenital heart defect in Hospital del Niño in San Juan while those on the island prepared for what would become one of the most catastrophic hurricanes in its history.
While he was still inside his mother’s womb, Luife was diagnosed with transposition of the great arteries, a congenital heart defect. Shortly after birth, Luife was taken by ambulance to the cardiac team at Nicklaus Children’s. The pediatric cardiology team took Luife’s heart apart, piece by delicate piece, and successfully, put it back together. Today, Luife is a healthy, active and outgoing 8-year-old boy who wears his “Scar of Honor” with pride.