Also known as: TA
What is Tricuspid Atresia?
In the normal heart, the tricuspid valve is the opening that controls the flow of blood between the right atrium (where the blood enters the heart) and the right ventricle (where the blood leaves for the lungs). Tricuspid atresia is a problem with the development of the right side of the heart where this valve has not developed, with a smaller than normal lower right pumping chamber (right ventricle). Because of this valve blockage to the flow of blood, the body receives blood with less oxygen in it than it needs. There is usually an associated hole between the right and left upper chambers of the heart (right atrium and left atrium) called an atrial septal defect.
What causes tricuspid atresia?
Tricuspid atresia is a defect that babies are born with (congenital birth defect). It is often present with other heart problems. The exact cause is not known.
What are the symptoms of tricuspid atresia?
Babies with tricuspid atresia will have a bluish or purple tint to their lips, skin and nails, shortness of breath, feed poorly, and be extremely fatigued.
What are tricuspid atresia care options?
Surgery is required to repair this defect as soon as possible. The baby may be given oxygen and a medicine called prostaglandin E1 to keep blood going to the lungs and require a breathing machine or ventilator before the surgery.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 6/12/2018 2:18:53 PM
The Heart Program at Nicklaus Children’s Hospital provides electrocardiogram (EKG) screenings to children and young adults in the community at no cost. The focus of this program is to create awareness on the importance of pediatric heart screenings in an effort to identify children at risk of sudden cardiac arrest (SCA). The use of an electrocardiogram (EKG) is critical to help diagnose asymptomatic heart defects that may not otherwise be detected in a routine physical. Learn more.