Total Anomalous Pulmonary Venous Return
Also known as: TAPVR
What is Total Anomalous Pulmonary Venous Return?
Ordinarily, oxygen-rich blood in the body enters the heart from the lungs through a series of four veins that feed into the left atrium ( the heart’s left upper chamber ) of the heart. With total anomalous pulmonary venous return, however, these veins from the lungs connect to other veins which eventually drain into the other upper chamber of the heart ( the right atrium ). The result is that the heart overworks and the body does not get the blood ( and the amount of blood with oxygen ) that it needs. The condition can be quite deadly in many instances.
What causes total anomalous pulmonary venous return?
Total anomalous pulmonary venous return is a defect that babies are born with (congenital birth defect). It is often present with other heart problems. The exact cause is not known.
What are the symptoms of total anomalous pulmonary venous return?
Babies with total anomalous pulmonary venous return will have a blue or purple tint to their lips, skin & nails, breath hard and rapidly especially when feeding and fatigue easily.
What are total anomalous pulmonary venous return care options?
Surgery is always required to repair this defect, critically ill babies will need it immediately; others as soon as possible.
Reviewed by: Jack Wolfsdorf, MD, FAAP
This page was last updated on: 6/12/2018 2:11:54 PM
From the Newsdesk
Naialee Perez had just given birth to her first child, a baby boy named Liam, when a category five hurricane was making its way towards her hometown in the island of Puerto Rico. Liam was on a ventilator and undergoing treatment for a congenital heart defect in Hospital del Niño in San Juan while those on the island prepared for what would become one of the most catastrophic hurricanes in its history.
While he was still inside his mother’s womb, Luife was diagnosed with transposition of the great arteries, a congenital heart defect. Shortly after birth, Luife was taken by ambulance to the cardiac team at Nicklaus Children’s. The pediatric cardiology team took Luife’s heart apart, piece by delicate piece, and successfully, put it back together. Today, Luife is a healthy, active and outgoing 8-year-old boy who wears his “Scar of Honor” with pride.