Long QT Syndrome (LQTS)

Also known as: long Q-T syndrome, LQTS

What is ​Long QT Syndrome (LQTS)?

There are many different types of abnormal heart rhythms, or arrhythmias. Long QT syndrome is an electrical problem of the heart that can lead to potentially dangerous arrhythmias which can present with a fainting spell, seizure or even sudden death.  It gets its name from an abnormal pattern on an EKG, which is a test of the heart’s electrical system.


What causes long QT syndrome?

This heart electrical problem may develop in several ways. It appears in many people to be related to a genetic mutation, or it can be passed down from parents to children. Other times, certain medications or other situations may cause long QT syndrome.


What are the symptoms of long QT syndrome?

The symptoms of long QT syndrome, as described above may occur suddenly & require urgent attention.


What are long QT syndrome care options?

Medications can help regulate heart rate in many with long QT syndrome. Other times, surgery to repair the heart or install a pacemaker might be an option. Some can help manage the condition with lifestyle changes such as avoiding stress, medications or extreme physical exertion.

Reviewed by: Jack Wolfsdorf, MD, FAAP

This page was last updated on: 3/23/2018 2:05:53 PM

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Ronald Kanter, MD of Nicklaus Children's Hospital is the Director of Electrophysiology with The Heart Program.


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