Long QT Syndrome (LQTS)

Also known as: long Q-T syndrome, LQTS

What is ​Long QT Syndrome (LQTS)?

There are many different types of abnormal heart rhythms, or arrhythmias. Long QT syndrome is an electrical problem of the heart that can lead to potentially dangerous arrhythmias which can present with a fainting spell, seizure or even sudden death.  It gets its name from an abnormal pattern on an EKG, which is a test of the heart’s electrical system.

What causes long QT syndrome?
This heart electrical problem may develop in several ways. It appears in many people to be related to a genetic mutation, or it can be passed down from parents to children. Other times, certain medications or other situations may cause long QT syndrome.

What are the symptoms of long QT syndrome?
The symptoms of long QT syndrome, as described above may occur suddenly & require urgent attention.

What are long QT syndrome care options?
Medications can help regulate heart rate in many with long QT syndrome. Other times, surgery to repair the heart or install a pacemaker might be an option. Some can help manage the condition with lifestyle changes such as avoiding stress, medications or extreme physical exertion.

Reviewed by: Jack Wolfsdorf, MD, FAAP

This page was last updated on: 6/12/2018 1:36:03 PM

From the Newsdesk

Infant flown from Puerto Rico days after Hurricane Maria for Lifesaving Surgery
Naialee Perez had just given birth to her first child, a baby boy named Liam, when a category five hurricane was making its way towards her hometown in the island of Puerto Rico. Liam was on a ventilator and undergoing treatment for a congenital heart defect in Hospital del Niño in San Juan while those on the island prepared for what would become one of the most catastrophic hurricanes in its history.
August Patient of the Month: Luife
While he was still inside his mother’s womb, Luife was diagnosed with transposition of the great arteries, a congenital heart defect. Shortly after birth, Luife was taken by ambulance to the cardiac team at Nicklaus Children’s. The pediatric cardiology team took Luife’s heart apart, piece by delicate piece, and successfully, put it back together. Today, Luife is a healthy, active and outgoing 8-year-old boy who wears his “Scar of Honor” with pride.