​Pulmonary Atresia (PA)

Also known as: PA

What is ​Pulmonary Atresia (PA)?

Pulmonary atresia is a birth defect of the heart where the valve that controls the flow of blood from the right side of the heart to the lungs  does not form, preventing blood picking up oxygen.


What causes pulmonary atresia? 

Pulmonary atresia is a congenital heart defect, which means that babies are born with it. Researchers aren’t sure of the exact cause, but it often occurs along with other heart problems such as patent ductus arteriosus or ventricular septal defect.


What are the symptoms of pulmonary atresia? 

Babies born with PA usually have symptoms at birth or soon afterwards. The lack of oxygen caused by pulmonary atresia leads to problems breathing and a blue tint to the skin. Sleepiness, fatigue & poor feeding also occur.


What are pulmonary atresia care options? 

Pulmonary atresia is a “ critical congenital heart defect”. Most babies will need medications to keep the ductus arteriosus open after birth to improve blood flow to the lungs. Surgical procedures will be needed to correct the defect.

Reviewed by: Jack Wolfsdorf, MD, FAAP

This page was last updated on: 6/12/2018 11:09:01 AM


Upcoming Events

Ventilation Assisted Children's Center (VACC) Camp

VACC Camp is a week-long sleep-away camp for children requiring ventilator assistance (tracheostomy ventilator, C-PAP, BiPAP, or oxygen to support breathing) and their families.  Learn more.

Register Online

From the Newsdesk

Li Travels all the way from Shanghai to Nicklaus Children’s for Management of his Complex Heart Condition
Li Hongyang, 37, traveled all the way from his hometown of Shanghai China to find the best possible care for his complex heart condition. What he did not expect is that he would receive his lifesaving treatment at a children’s hospital.
 
Dr. Redmond Burke Discusses Innovations in Cardiac Care Pioneered at Nicklaus Children's Hospital
Dr. Burke is the Pediatric Specialists of America (PSA) Chief of Cardiovascular Surgery with The Heart Program at Nicklaus Children's Hospital.